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Панникулиты в ревматологической практике
Панникулиты в ревматологической практике
Белов Б.С., Егорова О.Н., Савушкина Н.М. и др. Панникулиты в ревматологической практике. Consilium Medicum. 2016; 18 (12): 117–122. DOI: 10.26442/2075-1753_2016.12.117-122
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Аннотация
Под панникулитами понимают группу гетерогенных воспалительных заболеваний, характеризующихся поражением подкожной жировой клетчатки. Многообразие их форм и вариантов течения требует проведения тщательного обследования больного с целью верификации диагноза. В статье представлен диагностический алгоритм, изложены принципы дифференциальной диагностики и подходы к лечению панникулитов в современной ревматологической практике.
Ключевые слова: панникулиты, диагностика, дифференциальный диагноз, лечение.
Ключевые слова: панникулиты, диагностика, дифференциальный диагноз, лечение.
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Under panniculita the heterogeneous group of inflammatory diseases characterized by lesions of subcutaneous fat is understood. The variety of their forms and course options requires a careful examination of the patient for the purpose of verification of the diagnosis. The article presents a diagnostic algorithm, setting out the principles of differential diagnosis and treatment approaches to panniculita in modern rheumatology practice.
Key words: panniculitis, diagnosis, differential diagnosis, treatment.
Key words: panniculitis, diagnosis, differential diagnosis, treatment.
Полный текст
Список литературы
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15. Shen LY, Edmonson MB, Williams GP et al. Lipoatrophic panniculitis: casereport and review of the literature. Arch Dermatol 2010; 146 (8): 877–81.
16. Patterson JW. Panniculitis. In: Bolognia J.L., Jorizzo J.L., Schaffer J.V. (eds). Dermatology, Third Edition. Elsevier Limited, 2012; p. 1641–62.
17. Cusack CAR, Fanelli M. Panniculitis. In: Lebwohl M.G., Heymann W.R., Berth-Jones J., Coulson I.. (eds.) Treatment of Skin Disease: Comprehensive Therapeutic Strategies. Fourth Edition. Elsevier Limited. 2014; p. 526–31.
18. Narváez J, Bianchi MM., Santo P et al. Pancreatitis, panniculitis, and polyarthritis. Semin Arthritis Rheum 2010; 39 (5): 417–23.
19. Chee C. Panniculitis in a patient presenting with a pancreatic tumour and polyarthritis: a case report. J Med Case Reports 2009; 3: 7331.
20. Park HS, Choi JW, Kim BK, Cho KH. Lupusery the matosus panniculitis: clinicopathological, immunophenotypic, and molecular studies. Am J Dermatopathol 2010; 32 (1): 24–30.
21. Valverde R, Rosales B, Ortiz-de Frutos FJ et al. Alpha-1-antitrypsin deficiency panniculitis Dermatol Clin 2008; 26 (4): 447–51.
22. Саркоидоз. Уч.-метод. пособие. Под ред. А.А.Визеля, Н.Б.Амирова. Казань, 2010; с. 36–8. / Sarkoidoz. Uch.-metod. posobie. Pod red. A.A.Vizelia, N.B.Amirova. Kazan', 2010; s. 36–8. [in Russian]
23. Daher Ede F, Silva Júnior GB, Pinheiro HC et al. Erythema induratum of Bazin and renal tuberculosis: report of an association. Rev Inst Med Trop Sao Paulo 2004; 46 (5): 295–8.
24. Kirch W, Duhrsen U, Hoensch H et al. Cyclophosphamide-induced remission in Weber–Christian panniculitis. Rheumatol Int 1985; 5 (5): 239–40.
25. Martin RJ, Michals EL, Voth MR. Cyclophosphamide-induced remission in Weber–Christian disease: case report. Mil Med 1977; 142 (2): 158–60.
26. Szyszymar B, Gwiezdzinski Z. Treatment of recurrent panniculits febrilis nonsuppurativa with methotrexate. Przegl Dermatol 1974; 61 (5): 623–7.
27. Hotta T, Wakamatsu Y, Matsumura N et al. Azathioprine-induced remission in Weber–Christian disease. South Med J 1981; 74 (2): 234–7.
28. Al-Niaimi F, Clark C, Thorrat A, Burden A. Idiopathic lobular panniculitis: remission induced and maintained with infliximab. Br J Dermatol 2009; 161 (3): 691–2.
29. Mavrikakis J, Georgiadis T, Fragiadaki K, Sfikakis P. Orbital lobular panniculitis in Weber–Christian disease: sustained response to anti-TNF treatment and review of the literature. Surv Ophthalmol 2010; 55 (6): 584–9.
30. Егорова О.Н., Белов Б.С., Раденска-Лоповок С.Г. Лечение идиопатического панникулита Вебера–Крисчена. Материалы Х науч.-практ. конф. «Проблемы современной ревматологии». М., 2013; с. 185–8. / Egorova O.N., Belov B.S., Radenska-Lopovok S.G. Lechenie idiopaticheskogo pannikulita Vebera–Krischena. Materialy Kh nauch.-prakt. konf. “Problemy sovremennoi revmatologii”. M., 2013; s. 185–8. [in Russian]
2. Fittspatrik T.B., Bernard D.R. Kozhnye povrezhdeniia, imeiushchie obshchemeditsinskoe znachenie. V kn.: Braunval'd E., Issel'bakher K.Dzh., Petersdorf R.G. (red.). Vnutrennie bolezni. Kn. 2. Per. s angl. M: Meditsina, 1999; s. 67–82. [in Russian]
3. Diaz Cascajo C, Borghi S, Weyers W. Panniculitis: definition of terms and diagnostic strategy. Am J Dermatopathol 2000; 22 (6): 530–49.
4. Berenbein B.A., Studnitsin A.A. Differentsial'naia diagnostika kozhnykh boleznei. M.: Meditsina, 1989. [in Russian]
5. Ter Poorten MC, Thiers BH. Panniculitis. Dermatol Clin 2002; 20 (3): 421–33.
6. Requena L, Yus ES. Panniculitis. Part I. Mostly septal panniculitis. J Am Acad Dermatol 2001; 45 (2):163–83.
7. Requena L, Sanchez Yus E. Panniculitis. Part II. Mostly lobular panniculitis. J Am Acad Dermatol 2001; 45 (3): 325–61.
8. Verbenko E.V. Spontannyi pannikulit. V kn: Skripkin Iu.K. (red.) Kozhnye i venericheskie bolezni. Rukovodstvo dlia vrachei. T. 2. M.: Meditsina, 1995; s. 399–410. [in Russian]
9. Iwasaki T, Hamano T, Ogata A et al. Success ful treatment of a patient with febrile, lobular panniculitis (Weber–Christian disease) with oral cyclosporin A: implications for pathogenesis and therapy. Intern Med 1999; 38 (7): 612–4.
10. Lamprecht P, Moosig F, Adam-Klages S et al. Small vessel vasculitis and relapsing panniculitis in tumour necrosis factor receptor associated periodic syndrome (TRAPS). Ann Rheum Dis 2004; 63 (11): 1518–20.
11. Hinata M, Someya T, Yoshizaki H et al. Successful treatment of steroid-resistant Weber–Christian disease with biliary ductopenia using cyclosporin A. Rheumatology 2005; 44 (6): 821–3.
12. Egorova O.N., Belov B.S., Pushkova O.V., Volkov A.V. Pannikulity: voprosy diagnostiki. Consilium Medicum. Neurology and Rheumatology (Suppl.). 2013; 1: 42–7. [in Russian]
13. Goloeva R.G., Alekberova Z.S., Mach E.S. i dr. Sosudistye proiavleniia bolezni Bekhcheta. Nauchno-praktich. revmatologiia. 2010; 2: 51–7. [in Russian]
14. Thayalasekaran S, Liddicoat H, Wood E. Thrombophlebitis migrans in a man with pancreatic adenocarcinoma: a case report. Cases J 2009; 2: 6610.
15. Shen LY, Edmonson MB, Williams GP et al. Lipoatrophic panniculitis: casereport and review of the literature. Arch Dermatol 2010; 146 (8): 877–81.
16. Patterson JW. Panniculitis. In: Bolognia J.L., Jorizzo J.L., Schaffer J.V. (eds). Dermatology, Third Edition. Elsevier Limited, 2012; p. 1641–62.
17. Cusack CAR, Fanelli M. Panniculitis. In: Lebwohl M.G., Heymann W.R., Berth-Jones J., Coulson I.. (eds.) Treatment of Skin Disease: Comprehensive Therapeutic Strategies. Fourth Edition. Elsevier Limited. 2014; p. 526–31.
18. Narváez J, Bianchi MM., Santo P et al. Pancreatitis, panniculitis, and polyarthritis. Semin Arthritis Rheum 2010; 39 (5): 417–23.
19. Chee C. Panniculitis in a patient presenting with a pancreatic tumour and polyarthritis: a case report. J Med Case Reports 2009; 3: 7331.
20. Park HS, Choi JW, Kim BK, Cho KH. Lupusery the matosus panniculitis: clinicopathological, immunophenotypic, and molecular studies. Am J Dermatopathol 2010; 32 (1): 24–30.
21. Valverde R, Rosales B, Ortiz-de Frutos FJ et al. Alpha-1-antitrypsin deficiency panniculitis Dermatol Clin 2008; 26 (4): 447–51.
22. Sarkoidoz. Uch.-metod. posobie. Pod red. A.A.Vizelia, N.B.Amirova. Kazan', 2010; s. 36–8. [in Russian]
23. Daher Ede F, Silva Júnior GB, Pinheiro HC et al. Erythema induratum of Bazin and renal tuberculosis: report of an association. Rev Inst Med Trop Sao Paulo 2004; 46 (5): 295–8.
24. Kirch W, Duhrsen U, Hoensch H et al. Cyclophosphamide-induced remission in Weber–Christian panniculitis. Rheumatol Int 1985; 5 (5): 239–40.
25. Martin RJ, Michals EL, Voth MR. Cyclophosphamide-induced remission in Weber–Christian disease: case report. Mil Med 1977; 142 (2): 158–60.
26. Szyszymar B, Gwiezdzinski Z. Treatment of recurrent panniculits febrilis nonsuppurativa with methotrexate. Przegl Dermatol 1974; 61 (5): 623–7.
27. Hotta T, Wakamatsu Y, Matsumura N et al. Azathioprine-induced remission in Weber–Christian disease. South Med J 1981; 74 (2): 234–7.
28. Al-Niaimi F, Clark C, Thorrat A, Burden A. Idiopathic lobular panniculitis: remission induced and maintained with infliximab. Br J Dermatol 2009; 161 (3): 691–2.
29. Mavrikakis J, Georgiadis T, Fragiadaki K, Sfikakis P. Orbital lobular panniculitis in Weber–Christian disease: sustained response to anti-TNF treatment and review of the literature. Surv Ophthalmol 2010; 55 (6): 584–9.
30. Egorova O.N., Belov B.S., Radenska-Lopovok S.G. Lechenie idiopaticheskogo pannikulita Vebera–Krischena. Materialy Kh nauch.-prakt. konf. “Problemy sovremennoi revmatologii”. M., 2013; s. 185–8. [in Russian]
2. Фитцпатрик Т.Б., Бернард Д.Р. Кожные повреждения, имеющие общемедицинское значение. В кн.: Браунвальд Е., Иссельбахер К.Дж., Петерсдорф Р.Г. (ред.). Внутренние болезни. Кн. 2. Пер. с англ. М: Медицина, 1999; с. 67–82. / Fittspatrik T.B., Bernard D.R. Kozhnye povrezhdeniia, imeiushchie obshchemeditsinskoe znachenie. V kn.: Braunval'd E., Issel'bakher K.Dzh., Petersdorf R.G. (red.). Vnutrennie bolezni. Kn. 2. Per. s angl. M: Meditsina, 1999; s. 67–82. [in Russian]
3. Diaz Cascajo C, Borghi S, Weyers W. Panniculitis: definition of terms and diagnostic strategy. Am J Dermatopathol 2000; 22 (6): 530–49.
4. Беренбейн Б.А., Студницин А.А. Дифференциальная диагностика кожных болезней. М.: Медицина, 1989. / Berenbein B.A., Studnitsin A.A. Differentsial'naia diagnostika kozhnykh boleznei. M.: Meditsina, 1989. [in Russian]
5. Ter Poorten MC, Thiers BH. Panniculitis. Dermatol Clin 2002; 20 (3): 421–33.
6. Requena L, Yus ES. Panniculitis. Part I. Mostly septal panniculitis. J Am Acad Dermatol 2001; 45 (2):163–83.
7. Requena L, Sanchez Yus E. Panniculitis. Part II. Mostly lobular panniculitis. J Am Acad Dermatol 2001; 45 (3): 325–61.
8. Вербенко Е.В. Спонтанный панникулит. В кн: Скрипкин Ю.К. (ред.) Кожные и венерические болезни. Руководство для врачей. Т. 2. М.: Медицина, 1995; с. 399–410. / Verbenko E.V. Spontannyi pannikulit. V kn: Skripkin Iu.K. (red.) Kozhnye i venericheskie bolezni. Rukovodstvo dlia vrachei. T. 2. M.: Meditsina, 1995; s. 399–410. [in Russian]
9. Iwasaki T, Hamano T, Ogata A et al. Success ful treatment of a patient with febrile, lobular panniculitis (Weber–Christian disease) with oral cyclosporin A: implications for pathogenesis and therapy. Intern Med 1999; 38 (7): 612–4.
10. Lamprecht P, Moosig F, Adam-Klages S et al. Small vessel vasculitis and relapsing panniculitis in tumour necrosis factor receptor associated periodic syndrome (TRAPS). Ann Rheum Dis 2004; 63 (11): 1518–20.
11. Hinata M, Someya T, Yoshizaki H et al. Successful treatment of steroid-resistant Weber–Christian disease with biliary ductopenia using cyclosporin A. Rheumatology 2005; 44 (6): 821–3.
12. Егорова О.Н., Белов Б.С., Пушкова О.В., Волков А.В. Панникулиты: вопросы диагностики. Consilium Medicum. Неврология и Ревматология (Прил.). 2013; 1: 42–7. / Egorova O.N., Belov B.S., Pushkova O.V., Volkov A.V. Pannikulity: voprosy diagnostiki. Consilium Medicum. Neurology and Rheumatology (Suppl.). 2013; 1: 42–7. [in Russian]
13. Голоева Р.Г., Алекберова З.С., Мач Э.С. и др. Сoсудистые проявления болезни Бехчета. Научно-практич. ревматология. 2010; 2: 51–7. / Goloeva R.G., Alekberova Z.S., Mach E.S. i dr. Sosudistye proiavleniia bolezni Bekhcheta. Nauchno-praktich. revmatologiia. 2010; 2: 51–7. [in Russian]
14. Thayalasekaran S, Liddicoat H, Wood E. Thrombophlebitis migrans in a man with pancreatic adenocarcinoma: a case report. Cases J 2009; 2: 6610.
15. Shen LY, Edmonson MB, Williams GP et al. Lipoatrophic panniculitis: casereport and review of the literature. Arch Dermatol 2010; 146 (8): 877–81.
16. Patterson JW. Panniculitis. In: Bolognia J.L., Jorizzo J.L., Schaffer J.V. (eds). Dermatology, Third Edition. Elsevier Limited, 2012; p. 1641–62.
17. Cusack CAR, Fanelli M. Panniculitis. In: Lebwohl M.G., Heymann W.R., Berth-Jones J., Coulson I.. (eds.) Treatment of Skin Disease: Comprehensive Therapeutic Strategies. Fourth Edition. Elsevier Limited. 2014; p. 526–31.
18. Narváez J, Bianchi MM., Santo P et al. Pancreatitis, panniculitis, and polyarthritis. Semin Arthritis Rheum 2010; 39 (5): 417–23.
19. Chee C. Panniculitis in a patient presenting with a pancreatic tumour and polyarthritis: a case report. J Med Case Reports 2009; 3: 7331.
20. Park HS, Choi JW, Kim BK, Cho KH. Lupusery the matosus panniculitis: clinicopathological, immunophenotypic, and molecular studies. Am J Dermatopathol 2010; 32 (1): 24–30.
21. Valverde R, Rosales B, Ortiz-de Frutos FJ et al. Alpha-1-antitrypsin deficiency panniculitis Dermatol Clin 2008; 26 (4): 447–51.
22. Саркоидоз. Уч.-метод. пособие. Под ред. А.А.Визеля, Н.Б.Амирова. Казань, 2010; с. 36–8. / Sarkoidoz. Uch.-metod. posobie. Pod red. A.A.Vizelia, N.B.Amirova. Kazan', 2010; s. 36–8. [in Russian]
23. Daher Ede F, Silva Júnior GB, Pinheiro HC et al. Erythema induratum of Bazin and renal tuberculosis: report of an association. Rev Inst Med Trop Sao Paulo 2004; 46 (5): 295–8.
24. Kirch W, Duhrsen U, Hoensch H et al. Cyclophosphamide-induced remission in Weber–Christian panniculitis. Rheumatol Int 1985; 5 (5): 239–40.
25. Martin RJ, Michals EL, Voth MR. Cyclophosphamide-induced remission in Weber–Christian disease: case report. Mil Med 1977; 142 (2): 158–60.
26. Szyszymar B, Gwiezdzinski Z. Treatment of recurrent panniculits febrilis nonsuppurativa with methotrexate. Przegl Dermatol 1974; 61 (5): 623–7.
27. Hotta T, Wakamatsu Y, Matsumura N et al. Azathioprine-induced remission in Weber–Christian disease. South Med J 1981; 74 (2): 234–7.
28. Al-Niaimi F, Clark C, Thorrat A, Burden A. Idiopathic lobular panniculitis: remission induced and maintained with infliximab. Br J Dermatol 2009; 161 (3): 691–2.
29. Mavrikakis J, Georgiadis T, Fragiadaki K, Sfikakis P. Orbital lobular panniculitis in Weber–Christian disease: sustained response to anti-TNF treatment and review of the literature. Surv Ophthalmol 2010; 55 (6): 584–9.
30. Егорова О.Н., Белов Б.С., Раденска-Лоповок С.Г. Лечение идиопатического панникулита Вебера–Крисчена. Материалы Х науч.-практ. конф. «Проблемы современной ревматологии». М., 2013; с. 185–8. / Egorova O.N., Belov B.S., Radenska-Lopovok S.G. Lechenie idiopaticheskogo pannikulita Vebera–Krischena. Materialy Kh nauch.-prakt. konf. “Problemy sovremennoi revmatologii”. M., 2013; s. 185–8. [in Russian]
________________________________________________
2. Fittspatrik T.B., Bernard D.R. Kozhnye povrezhdeniia, imeiushchie obshchemeditsinskoe znachenie. V kn.: Braunval'd E., Issel'bakher K.Dzh., Petersdorf R.G. (red.). Vnutrennie bolezni. Kn. 2. Per. s angl. M: Meditsina, 1999; s. 67–82. [in Russian]
3. Diaz Cascajo C, Borghi S, Weyers W. Panniculitis: definition of terms and diagnostic strategy. Am J Dermatopathol 2000; 22 (6): 530–49.
4. Berenbein B.A., Studnitsin A.A. Differentsial'naia diagnostika kozhnykh boleznei. M.: Meditsina, 1989. [in Russian]
5. Ter Poorten MC, Thiers BH. Panniculitis. Dermatol Clin 2002; 20 (3): 421–33.
6. Requena L, Yus ES. Panniculitis. Part I. Mostly septal panniculitis. J Am Acad Dermatol 2001; 45 (2):163–83.
7. Requena L, Sanchez Yus E. Panniculitis. Part II. Mostly lobular panniculitis. J Am Acad Dermatol 2001; 45 (3): 325–61.
8. Verbenko E.V. Spontannyi pannikulit. V kn: Skripkin Iu.K. (red.) Kozhnye i venericheskie bolezni. Rukovodstvo dlia vrachei. T. 2. M.: Meditsina, 1995; s. 399–410. [in Russian]
9. Iwasaki T, Hamano T, Ogata A et al. Success ful treatment of a patient with febrile, lobular panniculitis (Weber–Christian disease) with oral cyclosporin A: implications for pathogenesis and therapy. Intern Med 1999; 38 (7): 612–4.
10. Lamprecht P, Moosig F, Adam-Klages S et al. Small vessel vasculitis and relapsing panniculitis in tumour necrosis factor receptor associated periodic syndrome (TRAPS). Ann Rheum Dis 2004; 63 (11): 1518–20.
11. Hinata M, Someya T, Yoshizaki H et al. Successful treatment of steroid-resistant Weber–Christian disease with biliary ductopenia using cyclosporin A. Rheumatology 2005; 44 (6): 821–3.
12. Egorova O.N., Belov B.S., Pushkova O.V., Volkov A.V. Pannikulity: voprosy diagnostiki. Consilium Medicum. Neurology and Rheumatology (Suppl.). 2013; 1: 42–7. [in Russian]
13. Goloeva R.G., Alekberova Z.S., Mach E.S. i dr. Sosudistye proiavleniia bolezni Bekhcheta. Nauchno-praktich. revmatologiia. 2010; 2: 51–7. [in Russian]
14. Thayalasekaran S, Liddicoat H, Wood E. Thrombophlebitis migrans in a man with pancreatic adenocarcinoma: a case report. Cases J 2009; 2: 6610.
15. Shen LY, Edmonson MB, Williams GP et al. Lipoatrophic panniculitis: casereport and review of the literature. Arch Dermatol 2010; 146 (8): 877–81.
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Авторы
Б.С.Белов*1, О.Н.Егорова1, Н.М.Савушкина1, Ю.А.Карпова1, С.Г.Раденска-Лоповок2
1 ФГБНУ Научно-исследовательский институт ревматологии им. В.А.Насоновой. 115522, Россия, Мсква, Каширское ш., д. 34А;
2 ФГБОУ ВО Первый Московский государственный медицинский университет им. И.М.Сеченова Минздрава России. 119991, Россия, Москва, ул. Трубецкая, д. 8, стр. 2
*belovbor@yandex.ru
1 ФГБНУ Научно-исследовательский институт ревматологии им. В.А.Насоновой. 115522, Россия, Мсква, Каширское ш., д. 34А;
2 ФГБОУ ВО Первый Московский государственный медицинский университет им. И.М.Сеченова Минздрава России. 119991, Россия, Москва, ул. Трубецкая, д. 8, стр. 2
*belovbor@yandex.ru
________________________________________________
B.S.Belov*1, O.N.Egorova1, N.M.Savushkina1, Yu.A.Karpova1, S.G.Radenska-Lopovok2
1 V.A.Nasonova Research Institute of Rheumatology. 115522, Russian Federation, Moscow, Kashirskoe sh., d. 34A;
2 I.M.Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation. 119991, Russian Federation, Moscow, ul. Trubetskaia, d. 8, str. 2
*belovbor@yandex.ru
1 V.A.Nasonova Research Institute of Rheumatology. 115522, Russian Federation, Moscow, Kashirskoe sh., d. 34A;
2 I.M.Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation. 119991, Russian Federation, Moscow, ul. Trubetskaia, d. 8, str. 2
*belovbor@yandex.ru
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